Questions of Diagnostics of Elastic Pseudoxanthoma

Elastic pseudoxanthoma is a hereditary disorder of the connective tissue, characterized by
calcifi cation of elastic fi bers, in various areas of the skin, eyes and cardiovascular system. Four known
forms of this disease are encoded by a dominant or recessive gene. As a rule, rash is visualized in
the secondfolds, neck, iliac crests, less often in the groin, umbilical region, or knee joints. Ophthalmic lesions
are manifested by angioid streaks and degenerative chorioretinal infl ammation (H30), leading to
blindness. Increased blood pressure, sudden cardiac death, stroke, or hemorrhagic syndrome are
the most common outcomes of cardiovascular damage in case of elastic pseudoxanthoma. decade of life and is manifested by small yellowish papules localized in the area of large